Case Report
Year: 2019 | Month: September | Volume: 9 | Issue: 9 | Pages: 252-255
Primary Sjogren’s Syndrome Presenting as Neuromyelitis Optica Spectrum Disorder (NMOSD)
Dr. Saranya. C
Assistant Professor, Department of Rheumatology, Sri Ramachandra Institute Of Higher Education and Research, Porur, Chennai
ABSTRACT
Primary Sjogren’s syndrome is a rare autoimmune disease characterised by keratoconjuctivitis sicca due to autoimmune destruction of exocrine glands. Neuromyelitis optica (NMO), is a severe, relapsing demyelinating disease that predominantly affects optic nerves and the spinal cord. NMO and related NMOSD have been found to be associated with Primary Sjogren’s syndrome. Here we report a patient who presented as Neuromyelitis optica spectrum disorder (NMOSD) and on evaluation found to have Primary Sjogren’s syndrome despite the absence of glandular symptoms. NMOSD as the initial presentation of Primary Sjogren’s syndrome is less frequently reported in the literature; hence this case has been reported.
Key words: Autoimmune disease, Neuromyelitis optica, demyelinating disease, optic nerves.