Case Report
Year: 2019 | Month: May | Volume: 9 | Issue: 5 | Pages: 429-432
Job’s Syndrome with Oral Manifestations- A Rare Case Report and Review of Literature
Dr Shalvi Vora1, Dr Freny Karjodkar2, Dr Kaustubh Sansare2, Dr Sunita Patankarv2
1Post Graduate Student, 2Prof. and Head,
Department of Oral Medicine, Nair Hospital Dental College, Mumbai
Corresponding Author: Dr Shalvi Vora
ABSTRACT
Job’s Syndrome also known as hyperimmunoglobulin E syndrome (HIES), is a rare primary immunodeficiency characterized by eczema, recurrent skin and lung infections, elevated serum IgE, and connective tissue and skeletal abnormalities. It is a multisystem disease affecting dentition, skeleton, connective tissues. Patients suffering from this syndrome may show characteristic facial appearance and many oral manifestations like high arched palate, depapillated tongue, variations in oral gingiva and mucosa. Here we present a rare case of Job’s syndrome in 12 year old boy having Characteristic Clinical features and rare Oral manifestations
Key words: Job’s Syndrome, Hyperimmunoglobulin E Syndrome, Ig E, Oral manifestations