Case Report
Year: 2017 | Month: January | Volume: 7 | Issue: 1 | Pages: 321-325
Multiple System Atrophy-Cerebellar Type (MSA-C): A Case Report
Mohd Abbas Ilyas, Pramod Shaha, Kulamani Sahoo, Rahul Khetawat, Gaurav Khairnar
Department of Radiodiagnosis: Krishna Institute of Medical Sciences, Karad, Maharashtra, India 415110.
Corresponding Author: Mohd Abbas Ilyas
ABSTRACT
Introduction: Multiple system atrophy (MSA) is a sporadic, progressive neurodegenerative disorder has clinical symptoms characterized by variable combination of Parkinsonism disease like symptoms, cerebellar ataxia & / or autonomic failure.
Presentation of Case: We describe one patient having cerebellar signs with MRI features predominant of MSA-C or olivopontocerebellar atrophy showing pontine “Hot cross Bun sign” with having unusual focal hemorrhages in bilateral globus pallidus.
Discussion: Striatonigral degeneration (MSA-P), characterized clinically by parkinsonian symptoms with degenerative changes predominantly affect basal ganglia, particularly the putamen. Shy-Drager syndrome (MSA-SDS) characterized by autonomic nervous system failure with somewhat variable pathologic changes, characterize by neuronal loss in the substantia nigra and the intermediolateral cell column of the spinal cord. Olivopontocerebellar atrophy (OPCA or MSA-C) characterized by predominantly by cerebellar signs, with predominant olivopontocerebellar atrophy.
Conclusion: We mainly draw attention to an uncommon case with predominant MSA-C signs& findings showing pontine “Hot cross Bun sign” having having unusual focal hemorrhages in bilateral globus pallidus.
Key words: Multiple system atrophy; olivopontocerebellar atrophy; Striatonigral degeneration; Shy-Dager Syndrome.